A Rare Case of Herlyn-Werner-Wnderlich Syndrome with an Ectopic Ureter and A Communication Between a Hydrocolpos and The Bladder Neck in A Uterus Didelphys.

1. Background
The HWW syndrome is clasified as a type III Müllerian disgenesia, that includes a uterus didelphys, a blind hemivagina and unilateral kidney agenesia [1]. Müller’s ducts migrate to the midline and merge together to form the uterus, cervix and upper vagina at around the 8th week of pregnancy. Incomplete or absent fusion will produce two uteri. Kidney agenesia generally follows Müller duct malformation. The incidence of uterus didelphys related to HWW is approximately 1/2000 to 1/28.000 [2]. The purpose of his case description is to offer a better understanding of HWW syndrome pathophysiology, especially in adult patients presenting with longstanding common and unspecific symptoms.